ASKIN tumor is a primitive neuroectodermal tumor of the chest wall, which is a rare small round cell tumor originating from the peripheral nervous system of the chest wall, with a high degree of malignancy and multidirectional differentiation potential.
ASKIN tumor grows rapidly, and its clinical manifestations are related to the size of the tumor and whether it invades the ribs and pleura; those involving the pleura are often accompanied by chest pain, and a large tumor compressing the lung tissues will easily lead to pulmonary atelectasis, pleural effusion, and obstructive inflammation.
ASKIN tumor imaging performance lack of characteristics, CT performance is now a large soft tissue mass in the chest wall, unclear borders, uneven density, there can be cystic changes and necrosis within the tumor, diagnosis of ASKIN tumor needs to rely on pathological diagnosis, pathologically, its characteristic performance for the Homer-Wright chrysanthemum-shaped doughnut-shaped structure.
In conclusion, in children or adolescents with large soft-tissue masses in the chest wall, uneven density, accompanied by osteogenic bone destruction of the ribs, we need to consider the possibility of this disease, and promptly consult the Department of Oncology, improve the examination, and make a clear diagnosis, so as to avoid delaying the treatment.