Diagnostic criteria for arrhythmogenic right ventricular cardiomyopathy

Arrhythmogenic right ventricular cardiomyopathy is currently diagnosed according to the TASK FORCE diagnostic criteria, which mainly summarize the clinical manifestations and characteristics of the disease according to six aspects of nine criteria, namely five major criteria and four minor criteria, and a patient is diagnosed with arrhythmogenic right ventricular cardiomyopathy when two major criteria or one major criterion plus two minor criteria are met, or when four different minor criteria exist. arrhythmogenic right ventricular cardiomyopathy. The six areas are: I. Local or global structural and functional alterations of the right ventricle. (ii) Ventricular wall tissue alterations. Abnormal repolarization. IV. Abnormalities of depolarization and conduction. V. Cardiac arrhythmias. Six, family history. Each of the six areas will be summarized with different primary and secondary criteria. For local or overall structural and functional changes of the right ventricle, it is necessary to assess whether there is severe dilatation of the right ventricle, whether there is a significant decrease in the ejection fraction of the right ventricle, or whether there is a ventricular wall tumor of the right ventricle and stage dilatation, mainly based on cardiac ultrasound or other imaging means. For ventricular wall tissue changes, myocardial or endomyocardial biopsy reveals that the myocardium has been replaced by fibrofatty tissue. Repolarization abnormalities or depolarization and conduction abnormalities are mainly based on the presence of T-wave inversions in leads V2 and V3 on the ECG, the presence of QRS wave widening in leads V1-V3, or the presence of Epsilon waves. In addition, arrhythmias are mainly based on the presence of left bundle branch block and frequent premature ventricular events. The most important criterion for family history is that the disease has been diagnosed in a family member after surgery or biopsy. A secondary criterion is a family history of sudden death in a family member before the age of 35, even though the diagnosis is not confirmed, or a family history of the disease can be diagnosed in a family member after this diagnosis. Therefore, the diagnosis of the disease is a comprehensive diagnosis and cannot be made by the performance of a single aspect.