Heterozygous cerebral leukodystrophy is the most common type of disease in the category of cerebral leukodystrophy. It is a deficiency of aryl sulfate esterase A activity that causes brain sulfolipid deposition in the body, resulting in extensive demyelination of the central nervous system, with the white matter of the brain being the most affected. Spherocytic cerebral white matter dystrophy is a disease in which galactosylcerebrosides are deposited in the brain due to a deficiency of beta-galactosidase. Adrenoleukodystrophy, characterized by progressive brain dysfunction with adrenocortical insufficiency, is a lipid metabolism disorder that is inherited and seen mainly in male patients. The main lesion is extensive demyelination of the white matter of the brain, spreading from the occipital to the frontal region, with the most pronounced damage in the parietal and temporal lobes. With the continuous development of MRI technology, many infants and children are examined with varying degrees of cerebral white matter dystrophy, and especially children with severe or more deafness are examined for cerebral white matter dystrophy before cochlear implant surgery, causing excessive parental concern. However, if the disease itself does not infringe on the temporal lobe auditory center, it has no direct effect on the hearing function and has no direct effect on the effect of cochlear implantation on hearing reconstruction. Parents do not need to over-interpret and over-worry, as active cooperation with surgery and good post-operative rehabilitation will give their children a wonderful world of sound.