Pachydermodactyly (PDD) is a rare benign fibromatosis. The name pachydermodactyly is derived from the Greek words pachy (thick), dermo (dermis) and dactylos (finger). Some call it collagen deposition in the proximal interphalangeal joint. PDD usually affects otherwise healthy young people. The evolution of joint swelling is insidious and it is more likely to develop bilaterally and symmetrically. Joints such as the distal interphalangeal joints are usually unaffected. The cause of PDD is unknown. In most cases, there is no family history or associated comorbidities. Some scholars believe that repeated minor trauma, or habitual or compulsive finger snapping due to finger breaking are predisposing causes. Because of the benign course of PDD, most patients do not require treatment. Some patients require treatment to correct the appearance of the deformity. Topical corticosteroid treatment is not effective. Some studies have shown that intra-lesional steroid injections may have some effect. Surgical excision or may improve the appearance but is rarely used.PDD is a rare benign condition and it is important to recognize and diagnose this condition without mistaking it for other diseases that can cause swelling of the soft tissues of the interphalangeal joints. Prompt diagnosis is needed to avoid unnecessary tests, reassure the patient, and avoid inappropriate treatment.