Ventricular meningeal cell tumors are CNS tumors that originate from ventricular meningeal cells in the ventricles and central canal of the spinal cord or from nests of ventricular meningeal cells in the white matter of the brain. According to the new 1993 WHO classification of CNS tumors, ventricular meningeal cell tumors are classified into four categories: ventricular meningioma, mesenchymal (malignant) ventricular meningioma, mucinous papillary ventricular meningioma, and subventricular ventricular meningioma. Ventricular meningiomas are low malignant and are equivalent to Kernohan grade I and II, while mesenchymal ventricular meningiomas are equivalent to Kernohan grade III and IV. The majority of mucinous papillary ventricular meningiomas are found in the cauda equina of the spinal cord. They are most commonly seen in children and young adults. Three quarters of the tumors are located subscopically and one quarter supratentorially, with a predominance of subscopically located tumors in children. Approximately 60% of supratentorial ventricular meningiomas in children originate in or contain tissue from the lateral ventricles and the wall of the three ventricles. The enlargement of the tumor often blocks the CSF circulatory pathway and causes a range of symptoms of high cranial pressure, including optic papilloedema, increased head circumference, lethargy, and headache and vomiting, while the remaining 40% of supratentorial ventricular meningiomas in children occur in the proximal cortical region and therefore cause symptoms such as hemiparesis and epilepsy. The most common location is the base of the four ventricles: about 60% of posterior cranial recess ventricular meningiomas occur at this site. It is noteworthy that most ventricular meningiomas at the base of the four ventricles originate from the ventricular membrane around the latch of the inferior horn of the four ventricles. In addition to increased intracranial pressure, patients often present with a sloping neck and ataxia; 2. 30% of subventricular ventricular tumors occur in the lateral saphenous fossa: the tumor grows intraventricularly as well as into the CPA, encircling and compressing the pontocerebrum and sloping anteriorly downward to the medulla oblongata. Patients often have posterior cranial nerve symptoms: hearing impairment, dysarthria, dysphagia, and poor distance discrimination; 3. Ataxia may occur when the earthworm is compressed. Treatment: Regardless of intracranial or spinal ventricular meningioma, total surgical excision is the best option, but because the tumor can invade the brainstem and encircle the cranial nerves, the rate of total surgical excision is less than 50%. Radiotherapy is effective for surgical residual tumors, and ventricular meningioma is moderately sensitive to radiotherapy. The use of high-dose fractionated radiotherapy above 65 Gy can improve the survival rate of patients with near-total resection. Chemotherapy is not effective for ventricular meningioma, but postoperative chemotherapy may be an option for infants and children to slow tumor growth while waiting for radiotherapy. Postoperative radiotherapy should be given for interstitial ventricular meningioma.