In a recent clinic visit, we have seen several children with sudden deafness who have been treated by several hospitals with unsatisfactory results. Idiopathic sudden deafness in children is uncommon and usually there are developmental malformations that lead to the occurrence of deafness under the action of external factors. As a parent, it is important to go to a regular hospital with a doctor who has some experience when you find a problem with your child’s hearing to avoid delaying the condition. Idiopathic sudden deafness in children is often a symptom, and the real cause is a developmental malformation, such as large vestibular aqueduct syndrome. In addition to active clinical treatment, the cause should be sought to combine prevention and treatment in order to benefit the hearing of the affected child.