Inferior tricuspid valve malformation, also known as Ebstein’s malformation, is a partial or complete downward shift of the tricuspid valve annulus into the right ventricular cavity, accompanied by malformation of the tricuspid valve membrane and structural changes in the right ventricle. It may be associated with other malformations such as patent ductus arteriosus, atrial septal defect, ventricular septal defect, and tetralogy of Fallot. It is a rare congenital heart malformation, the incidence of which is about 0.5%-1% in congenital heart disease, and the incidence is similar in both sexes. The surgical correction of Ebstein’s malformation mainly includes tricuspid valve repair or replacement, folding of atrialized ventricles, closure of atrial septal defects, as well as the management of combined cardiovascular malformation lesions, such as electrophysiologic localization of bypass conduction for preexcitation syndrome, and right maze surgery for chronic atrial fibrillation. The specific surgical approach depends on the patient’s condition. 1, palliative surgery Ebstein malformation palliative surgery called superior vena cava and right pulmonary artery anastomosis (modified Gleen operation) In infancy, such as severe cyanosis, hypoxemia, heart failure can not be controlled by medical treatment, the implementation of corrective surgery is difficult, sub-operative section to reduce the right heart load, reduce the right to left shunt, increase the arterial oxygen content, can improve the symptoms, reduce cyanosis and heart failure. Obtain postponement effect, to create time and conditions for future corrective surgery. (1) Tricuspid valvuloplasty (Danielson and Carpentier procedures) Tricuspid valvuloplasty consists of reconstructing the displaced tricuspid spiral in the normal oval atrioventricular ring, reducing the enlarged atrioventricular ring, folding and suturing to eliminate the “atrialized right ventricle,” and closing the septal defect. Repair of incomplete valves when needed. Danielson procedure: This is a commonly performed procedure. A reconstructed tricuspid valve is created using the anterior leaflet of the tricuspid valve, and the free wall of the left ventricle of the “atrialized right ventricle” is partially collapsed to create a superiorly displaced tricuspid annulus and reduce the size of the right atrium. Carpentier procedure: Carpentier procedure affects the function of the right ventricle to some extent and risks distorting the right coronary artery, especially if the “atrialized right ventricle” is removed, which may damage the right coronary artery. The advantage of the Carpentier procedure is that the geometry of the right ventricle from the apex to the base is maintained by always trying to collapse the “atrialized right ventricle,” and the tricuspid annulus is reduced, thus preserving the morphology and function of the right ventricle. (2) Valve replacement If the free edge of the tricuspid valve is attached to the right ventricular wall or if the structure of the tricuspid valve is completely unclear or even if there is no tendon or papillary muscle, then the prosthetic valve is replaced. Pediatric prosthetic valve replacement is advisable with mechanical valves because although biological valves do not require lifelong anticoagulation, it is advisable to have calcification and valve failure within a short period of time after surgery; the possible reasons are that pediatric calcium metabolism is higher than that of adults and susceptibility to infection, which leads to calcium salt deposition, and that the durability of biological valves is not as strong as that of mechanical valves to avoid the concern of valve replacement again. (3) Total vena cava-pulmonary artery connection is indicated in cases of severe right ventricular dysplasia, for which all of the above procedures are inappropriate.