1. Which age group of children with PKU are suitable for PKU milk powder and protein powder?
Phenylalanine-free milk powder basically contains all kinds of nutrients needed by infants, but the protein content is low, mainly for PKU children within 1 year old; while protein powder without phenylalanine has high protein content, but other nutrients should be supplemented through other diets, mainly for PKU children over 1 year old.
2.How to supplement vitamins and trace elements for children with phenylketonuria (PKU)?
In general, a sufficient daily supply of fruits and vegetables can meet the needs of children with phenylketonuria (PKU) for vitamins and trace elements, while fruits and vegetables rich in fiber can adjust the function of the intestinal tract and correct constipation.
3.How to choose sweeteners for children with phenylketonuria (PKU)?
Phe is the main ingredient of some artificial sweeteners. Such as sweetener, aspartame, meringue, etc. So drinks, candies and pastries containing artificial sweeteners with phenylalanine should not be consumed. Honey contains 44mg/100g of phenylalanine, which can be used according to the calculated amount.
4.Phenylketonuria patients with dietary control need to how old do they need to be?
The earlier the dietary control of phenylketonuria, the better. Low phenylalanine dietary treatment should be continued at least until the maturity of puberty, and lifelong treatment is advocated. After pubertal maturity, high levels of phenylalanine can still have an impact on mental mood if eaten at will.
5.What is the prognosis of phenylketonuria?
If children with phenylketonuria are not treated or treated late, most of them have mental developmental delays, such as motor and speech impairment. Through neonatal disease screening, children with phenylketonuria can be detected early and treated in a timely and regular manner, and nearly 90% of children with phenylketonuria can reach the intelligence of normal children of the same age.
6.How to choose food for children with phenylketonuria?
At present, there are domestic and imported formula powder without phenylalanine or low phenylalanine (commonly known as special milk powder), as well as rice, noodles, pasta and cookies without phenylalanine or low phenylalanine available for parents to choose. Natural foods such as breast milk is the best low-phenylalanine food; vegetables, fruits, melons, sugars and fats are foods that can be consumed freely; dairy, beans and cereals, which contain a certain amount of phenylalanine, are foods that need to be controlled; meat, fish and eggs, which are high-quality proteins, can be consumed with caution under the guidance of a doctor; seafood, cheese and offal, which contain high levels of phenylalanine, are usually Do not choose the food.