Nasal extranodal NK/T-cell lymphoma is a non-Hodgkin’s lymphoma originating from mature NK cells and NK-like T cells that has a close association with EBV infection, with the initial lesion in the nasal cavity in approximately 90% of patients. There are significant geographical differences in the distribution of the disease globally, with it being rare in Europe and the United States and more common in East Asia and South America. Statistics from a larger sample indicate that nasal extra-nodal NK/T-cell lymphoma is the most common lymphocytic neoplasm after diffuse large B-cell lymphoma in China, accounting for 11.0% of all lymphocytic neoplasms, 12% of non-Hodgkin’s lymphomas, and 8.8% of all lymphomas in children. In Korea, nasal-type extra-nodal NK/T-cell lymphoma accounts for only 3.9% of lymphocytic neoplasms. Therefore, nasal type extra-nodal NK/T-cell lymphoma is not a rare disease, but a more common lymphoma. On average, one in 10 lymphoma patients in China has nasal extra-nodal NK/T-cell lymphoma, which is the second most common lymphoma subtype.