Congenital absence of the vagina, also known as vaginal atresia, is a relatively rare congenital anomaly caused by the failure to extend caudally to form a vagina after the confluence of the bilateral paramedian ducts during embryonic development. It is often combined with congenital absence of the uterus or a dysplastic uterus, or even a congenital urinary anomaly, but with normal ovarian development, good secondary sexual characteristics, and rarely a well-developed uterus. There are two types of congenital anovagina, complete and incomplete, the former being more common. The former is more common. Most of them are seen in adolescence when there is no menstrual flow, or only periodic lower abdominal distension, or when married people cannot have sexual intercourse.