Corneal dermatomas are a relatively common tumor-like congenital abnormality in infants and young children, and are not true tumors histologically, but are typical mydriasis. The surface of the mass is covered with epithelium, and the mass consists of fibrous and fatty tissue, and may also contain hair follicles, hairs, and sebaceous and sweat glands. The lesion usually invades the superficial layer of the corneal parenchyma and occasionally reaches the entire corneal layer or even the anterior chamber. The swelling is usually present at birth and increases slightly with age and ocular development. Most of them are located in the temporal inferior part of the corneosclera, and a few may invade the whole cornea. The external appearance is skin-like, with clear borders and may have the presence of delicate hairs. Larger ones can often cause corneal astigmatism and vision loss. Surgical excision is the main treatment. For more superficial masses, direct excision can be performed, while larger masses or masses accumulating in the corneal stroma can be combined with lamellar corneoscleral transplantation at the same time. For children, the surgery should be performed under general anesthesia, and the postoperative period should be considered according to the size of the tumor and the surgical situation, whether it should be done locally or in combination with systemic immunosuppressive drugs.