A 3-month-old male with a yellowish-white mass on the lower part of his left eyeball, which grew rapidly and gradually covered most of the cornea, was admitted to our hospital. He was admitted to our hospital on February 20, 2005 with the diagnosis of “left corneal dermatoid tumor”. Examination: the skin of both upper and lower lids was not red and swollen, and the skin moved freely. A hemispherical swelling protruded 10mm forward and outward from the lower part of the left cornea, which was pink in color, and protruded outside the eyelid fissure, with neovascularization on its surface, occupying 2/3 of the area of cornea and a part of the corneal rim of the outer conjunctiva, and the root of the tumor had a diameter of 7mm, and a yellow-white confined swelling was seen in the right corneal rim of the corneal rim of the right cornea in the position of 7:0, with an approximate size of 2×2mm. Oral examination: facial asymmetry, deformity of the lower 1/3 of the face, the left corner of the mouth to the level of the left buccal part of the whole layer of exclusion, wider than the healthy side of the corner of the mouth 1.5 cm, no deformity of the upper and lower jaws, opening and closing the mouth is normal. Ear examination: both auricles were normal, with -1×0.5×0.5cm appendages 0.5cm from the ear screen in front of the right ear screen, and -1.5×1.5×0.7cm appendages 0.8cm from the ear screen in front of the left ear screen. The child underwent left corneal dermatoid tumor excision, corneal laminectomy, and left facet transverse fissure repair under compound anesthesia on February 22, 2005, and the postoperative pathological diagnosis of the excised mass was corneal dermatoid tumor. Li Xiaodong, Department of Ophthalmology, Baicheng Central Hospital, discussed: Corneal dermatoid tumor is a kind of tumor caused by congenital developmental abnormality, which mostly occurs in the corneal limbus of the temporal region of the globe, and develops in one eye or both eyes, and is often accompanied by other congenital abnormality, such as attached ear, preauricular fistula, and eyelid defects. When young, the tumor is small and limited, grayish-yellow or pinkish-red elevated, and the surface resembles skin. Ocular irritation can occur if there is hair growth on the surface. The tumor grows with age, and after entering school age, the growth accelerates, often violating the pupil area and affecting vision. The patient in this case had congenital keratodermatoid tumor in both eyes. The tumor in the right eye was small and limited, and the surface of the tumor in the left cornea was covered with neovascularization, and a few cilia could be seen under the operating microscope. The tumor grew rapidly, and occupied 2/3 of the corneal area in the first 3 months of life, and was combined with bilateral epiphora and the left facet transverse fissure, which was really rare.