Primitive neuroectodermal tumors are highly malignant tumors, which are theoretically curable, but clinically very unlikely to be cured. Primitive neuroectodermal tumors originate from primitive nerve bodies and are highly invasive, easily disseminated, fast-growing, and come in a variety of types, such as medulloblastomas, but they are rare. Central primitive neuroectodermal tumor belongs to a kind of highly malignant tumor, the growth mode has the characteristic of invasive growth, and it can even be disseminated and proliferated by shedding tumor cells in the cerebrospinal fluid circulation, and it often manifests itself as multiple implanted tumors in the intracranial vertebral canal. Because of its high malignancy and rapid proliferation and dissemination, it may not be completely eradicated after timely surgery, so the cure rate is low.