He was admitted to the hospital with an outpatient cardiac ultrasound indicating severe pulmonary hypertension with ventricular septal defect and endocardial elastin fibroplasia to be excluded. After hospitalization, the diagnosis of severe aortic constriction, ventricular septal defect and unclosed ductus arteriosus with severe pulmonary hypertension was confirmed by repeat cardiac ultrasound and 64-row CT. After preoperative preparation, the aortic stenosis, ventricular septal defect and unclosed ductus arteriosus were corrected in one stage through a median thoracic incision under extracorporeal circulation, and the blood pressure in the upper and lower extremities was equal after the operation.