Congenital myotonic squamous neck is a squamous neck due to contracture of the sternocleidomastoid muscle on one side. In the first 2 weeks after birth, a round or oval hard lump can be felt in the neck, which can grow to the size of a date palm in 1 to 2 months. After that, it will gradually become smaller or disappear within 2 to 3 months. Due to the pulling of the sternocleidomastoid muscle, the neck is skewed and the head is tilted to the affected side, while the jaw is turned to the healthy side, forming a special postural deformity. If left untreated, various secondary deformities may occur, including facial asymmetry, low eye and ear plane on the affected side, small eye fissure, and compensatory scoliosis of the cervical spine. Rotation of the head and neck to the affected side and tilt to the healthy side are limited. Early diagnosis and early treatment, with simple methods and excellent efficacy, are the keys to prevent the emergence of secondary deformities. Non-surgical treatment: When a cervical mass is found in the neonatal period, under the guidance of a physician, the parents should perform passive neck pulling activities for the child, fixing the shoulder on the affected side with one hand and gradually pulling the head and neck to the healthy side first, then turning the lower jaw to the affected side with the other hand. In addition, the affected side is fixed on the mother’s chest while breastfeeding so that the affected side is pulled. When teasing the baby, standing on the affected side is also a way to pull the sternocleidomastoid muscle. The swelling can also be gently massaged. Most of them can be cured by non-surgical treatment, and about 86% of them have satisfactory results. Surgical treatment: Children over 1 year old who have been treated conservatively for half a year to a year and have not been treated can only have their deformities corrected by surgery because the muscles have become fibrotic and the face is deformed. The best age for surgery is 1-5 years old. 5-12 years old and above, because of the secondary deformity is heavier, facial deformation is more difficult to recover, but through surgery, can still hope to obtain a significant part of the correction of deformity, should not take the attitude of giving up treatment. The following surgical methods are often used: sternocleidomastoid muscle clavicle head and sternocleidomastoid head cut release, sternocleidomastoid muscle Z-shaped lengthening surgery. Postoperative treatment: cervical brace or orthopedic brace should be fixed for 4-6 weeks, if over 6 years old, the head should be fixed in the overcorrected position, and those under 2 years old should insist on daily passive head and neck exercises in order to maintain the range of motion of the head and neck. (A) congenital myotonic neck on the right side; (B) fixing the affected shoulder with one hand and pulling the head and neck toward the healthy side with the other hand; (C) turning the lower jaw to the affected side; (D) dissection of the right sternocleidomastoid muscle.