Fibrosarcoma in infants and children is a very rare malignancy that occurs in infants and children but rarely metastasizes. Almost all children are less than 1 year old, and approximately 36-80% of patients have congenital disease, meaning that they are born with fibrosarcoma. The tumor tends to develop in the distal part of the limb, and the tumor can be relatively superficial or located deep. Most present as isolated masses that grow rapidly, even so large that they are out of proportion to the child’s body. The surface of the tumor may appear red or even rupture. Infantile fibrosarcoma has more specific chromosomal abnormalities. The prognosis for infantile fibrosarcoma is good, with an overall metastasis rate of less than 5%. However, some patients can develop local recurrence. The literature reports cases of patients who do not recur even with incomplete resection, and even cases of spontaneous regression. Patients with recurrence or incomplete surgical resection can be treated with VAC regimen chemotherapy.