Congenital spinal cord cavernosis is a very serious disease caused by congenital factors. Due to various reasons in the embryonic period, after birth, the child’s atlanto-occipital region has a narrower cranial development, resulting in intracranial subcerebellar herniation of the cerebellar tonsils to the position of the occipital foramen magnum, resulting in cerebrospinal fluid circulation obstacles, patients with spinal cord cavitation, resulting in symmetrical, isolated sensory disorders. Early symptoms of the patient is the appearance of limb sensory impairment, especially the double upper limb pain and temperature sensory impairment, that is, the patient to the temperature, pain sensory loss. If further development occurs, limb weakness will appear, and muscle atrophy or even clawed hands may appear if the disease continues to develop. If the spinal cord cavity is not treated, further development may cause the patient to develop urinary and bowel disorders, and in severe cases, paralysis may occur. Patients with spinal cord cavernous disease should be detected, diagnosed and treated early. More than 90% of patients can get symptomatic relief after regular surgical treatment in regular hospitals when discovered early; if discovered late, the treatment effect will be poorer. Because nerve cells cannot be regenerated, doctors can only perform decompression surgery on the basis of the disease at a later stage, and nerve function cannot be restored. Although this disease is common, it also needs to be paid great attention to, in order to provide space for the surgeon to treat the disease, and to do the corresponding surgery within the limited space, in order to achieve a more satisfactory result.