The severity of pulmonary vascular malformation needs to be considered according to the actual malformation and clinical manifestations. In some cases, no treatment is needed as there are no symptoms; in others, due to the severity of the malformation and its impact on respiratory and circulatory functions, the condition is serious and requires early treatment such as relevant orthopedic surgeries. Pulmonary vascular malformations are generally caused by congenital developmental abnormalities, and different malformations may lead to different clinical symptoms. Some patients have only minor pulmonary vascular malformations that do not affect them and do not require treatment; others have malformations that seriously affect cardiopulmonary function from the beginning, or symptoms that appear slowly during development, which have a great impact on the quality of life and may even be fatal. It is recommended that the severity of pulmonary vascular malformations be assessed by a specialized physician in a specialized institution, and even if there are no symptoms for a short period of time, regular follow-ups should be conducted to avoid progression of the disease, and it is recommended that the physician give tailored guidance and advice.