Neuroendocrine carcinoma of the uterine cervix is a rare type of cervical cancer, originated from neuroendocrine cells, with strong invasiveness and extremely poor prognosis, and should be treated as early as possible. Cervical neuroendocrine carcinoma is a rare cervical malignant tumor, accounting for only 1% of cervical cancer. It also belongs to malignant neuroendocrine tumors, originated from neuroendocrine cells (APUD cells), and can be classified into four categories: small cell carcinoma, large cell carcinoma, typical carcinoid tumor and atypical carcinoid tumor. Neuroendocrine carcinoma of the cervix mostly manifests as vaginal bleeding and drainage, pelvic pain and pelvic pressure symptoms, while paraneoplastic syndrome is less common, and its diagnosis depends on pathological and immunohistochemical examination. Cervical neuroendocrine carcinoma requires comprehensive treatment. Early stage tumors can be treated with radical surgery, radiotherapy, chemotherapy and selective neoadjuvant chemotherapy; locally advanced tumors can be treated with systematic radiotherapy and chemotherapy; distant metastatic tumors can be treated with palliative therapy. The prognosis of cervical neuroendocrine carcinoma is extremely poor, and it is easy to have lymphatic metastasis and distant metastasis, so it is recommended that patients suspected of having this disease should consult the doctor as early as possible for examination and active treatment.