Coronary arteriopulmonary fistula is a congenital condition that is caused by abnormal traffic between the coronary arteries and the heart chambers or lumen, and can be diagnosed due to the widespread use of cardioplegia and selective coronary angiography. Coronary pulmonary arteriovenous fistulae form for different reasons than normal congenital heart disease. It may be the result of a viral infection of the pregnant mother, the malnourished uterus under the influence of certain physicochemical factors or genetic factors. Its hemodynamic impact is mainly determined by the size of the fistula and the location of the fistula. Usually, coronary pulmonary artery fistulae have very little blood flow and the patient does not have any particular presenting symptoms. However, if it is a large flow, it may also cause some symptoms of the patient, such as heart enlargement, causing left ventricular enlargement and hypertrophy, dilatation of the ascending aorta, and may even cause heart failure, therefore, whether to treat it or not depends on the severity of the condition. Patients are advised to visit the hospital in time and take appropriate treatment measures under the guidance of physicians.