Developmental venous malformations usually refers to cerebral developmental venous malformations, a congenital disorder. Developmental venous malformations (DVAs), which may also be referred to as cerebral venous malformations or hemangiomas, are a rare form of intracranial vascular malformation. Developmental venous malformations are lesions that connect two large superficial and deep veins at the medullary veins of the brain to maintain a balanced drainage. However, when one of these drains is impaired, the medullary vein dilates, causing venous blood to return from the other system. Developmental venous malformations of the brain are not clinically obvious, but in a few cases they may be characterized by epilepsy, minor hemorrhages or neurological dysfunction or even facial hemangiomas. Developmental venous malformations are treated in the same way as other cerebrovascular malformations, with asymptomatic patients being observed closely and treated conservatively. When symptoms appear, or the risk of cerebral hemorrhage is high, surgical resection is performed.