Familial exudative vitreoretinopathy is a lifelong disease that impairs visual function and has a poor prognosis for vision in severe cases, with Stage III being the more severe form of the disease.
Familial exudative vitreoretinopathy is one of the blinding ophthalmic diseases in children and is clinically categorized into five stages. Stage III is a more severe condition with clinical manifestations of tractional and/or foraminal non macular retinal detachment with or without exudation that can significantly impair the patient’s vision. Patients may be relieved of the traction by means of ring ligation or vitreous surgery.
Familial exudative vitreoretinopathy is an inherited retinal vascular disease that threatens the vision of children and should be diagnosed early and treated appropriately.
Family members of patients with familial exudative vitreoretinopathy are advised to visit hospitals for screening, which can help identify asymptomatic carriers and also help diagnose the disease to avoid underdiagnosis and misdiagnosis.