Caudal chordoma is clinically known as caudal chordoma, which is mainly treated by surgery, often supplemented by radiotherapy and targeted therapy. 1. Sacrococcygeal chordoma is a low malignant tumor that occurs in the sacrococcygeal region, which is the residual spinal cord tissue of the embryo, and the etiology of the tumor is not completely clear. For patients with sacrococcygeal chordoma, it often manifests as chronic low back and leg pain, as well as mechanical obstruction of urination and defecation, and a mass can be detected during anus examination. 2. Surgical resection of the tumor is the main treatment method. Most of the patients with nerve preservation can be cured, and the recurrence rate is 20%. For patients with low malignancy, lung metastasis is rare. 3. The treatment of patients with sacrococcygeal chordoma is based on comprehensive treatment, including surgery, radiotherapy, chemotherapy, interventional therapy and so on. Through comprehensive treatment, it can reduce local recurrence, inhibit tumor growth and prolong the survival time of patients. If diagnosed with caudal chordoma, early standardized treatment is recommended to reduce the adverse effects of the disease.