Congenital spinal cord embolism syndrome is a congenital disorder that occurs in newborns and is caused by abnormal development of the nerve root canal during intrauterine embryonic development, which eventually causes the nerve to develop faster than the spinal canal and leads to a series of clinical symptoms. The common symptoms of congenital spinal cord embolism syndrome are pain and sensory deficits, as well as motor abnormalities, especially bilateral weakness of the lower extremities for walking. In congenital spinal cord embolism syndrome, skin sensory abnormalities in the saddle area are common, and in severe cases, contractile and diastolic dysfunction of the bladder and rectum, including enuresis, urinary frequency, urinary incontinence, and urinary retention.