1.The annual incidence of bilateral acoustic neuroma is about 1/100,000, accounting for about 4% of the acoustic nerve Schwann’s cell tumor, which is the main combined tumor of neurofibromatosis type II in the skull. 2.Hearing impairment is often bilateral, with one side being the heaviest, often combined with intracranial meningioma and other intracranial tumors, a few have skin “coffee spot”, skin, subcutaneous tissue, peripheral nerves can be seen in multiple neurofibromatosis nodules. The key to treatment is to preserve facial nerve and effective hearing on at least one side. Generally, staged surgical treatment is required, and generally the larger side of the acoustic neuroma is surgically removed first to relieve the increased intracranial pressure and hydrocephalus.