Embolism is a clinical condition in which the teeth grow in the shape of an embolism due to certain diseases. Embolism is one of the clinical manifestations of pediatric dyschromia. Incontinentiapigmenti is also known as incontinentia pigmentosa, Bloch-Sulzberger syndrome, Bloch-Siemens syndrome, dermal degenerative melanosis (melanosiscoriadegenerarativa). It is a rare complex genetic syndrome with characteristic skin changes that can be associated with ocular, skeletal, and central nervous system malformations and abnormalities. Pediatric achromatopsia is an inherited disorder, predominantly seen in females, and is an X-linked dominant disorder now confirmed to be caused by mutations in Xq11 (IP1) and Xq28 (IP2) localized to the long arm of the X chromosome. Mutations in the nuclear factor NF-kB gene regulator (NEMO) gene play a role in the inhibition of tumor necrosis factor-induced apoptosis, suggesting that it is responsible for the development of this disease. Patients present with urticaria-like, blister-like, and verrucous dermatitis changes on both sides of the trunk about 2 weeks after birth. A secondary pigmented maculopapular rash often develops on the trunk, upper arms, and thighs. The pigmentation is paprika-like or fountain-like, and the damage is not distributed along the dermatomes or nerves. The pigmentation may last for several years, fading without leaving marks, or leaving pale depigmented spots. The skin lesions of this disease sign can be clinically divided into 3 stages Stage I: erythema and blisters, arranged in rows, present at birth or significant within 2 weeks after birth, often affecting the limbs and trunk, not involving the face; Stage II: hyperkeratotic warty rash and plaques consisting of lesions, seen in 2/3 of the patients, which are secondary to blisters and appear in the same area of the skin rash. The warty lesions resemble linear epidermal naevi, and these usually disappear by 1 week of age, with a few persisting for several years. There is widely spread, irregularly distributed or swirling pigmentation. Stage III: Peculiar reticular hyperpigmentation, most prominent in the trunk damage. Typically there is hyperpigmentation at the nipples, and the inguinal and axillary pigmentation is most characteristic. Other cutaneous changes include pseudobaldness, chronic atrophic acrodermatitis-like skin atrophy, nail atrophy, nail dystrophy, subungual tumors with subungual osteolytic lesions, and palmoplantar hyperhidrosis. 70% to 80% of the patients have extracutaneous manifestations, most often involving the teeth, central nervous system, eyes, and skeleton.