Dopa-responsive dystonia testing generally involves the use of small doses of dopa preparations on patients to monitor the effectiveness of their treatment. Dopa-responsive dystonia is a chromosomal dominant disorder with reduced dopamine levels, which is usually normal when blood tests, cerebrospinal fluid tests, and liver function tests and imaging tests are done and cannot be directly diagnosed by testing. Patients with dopa-responsive dystonia are treated with dopamine preparations with significant results and good symptomatic relief. Therefore, the diagnosis of the disease is usually made by observing the patient’s results of treatment through clinical symptoms and the use of small dosages of dopa preparations, and by ruling out other diseases in combination with a number of common tests. If dopa-responsive dystonia is suspected, one should actively cooperate with the examination and treatment for early diagnosis.