Hemophagocytic syndrome is a rapidly progressive and highly lethal disease that has the potential to be cured, but it depends on the primary disease, the early or late diagnosis, and the patient’s tolerance level.
Hemophagocytic syndrome is a severe inflammatory response syndrome due to abnormalities in immunoregulatory function, with a variety of underlying etiologies and multidisciplinary aspects, and is a rapidly progressive and highly lethal disease. Whether it is curable depends on the patient’s response to treatment, tolerance level, and other conditions.
Treatment of hemophagocytic syndrome is divided into an induced remission phase to control the progression of the activation of the inflammatory state, and etiologic treatment for the primary disease, along with systemic supportive therapy for infection, hemorrhage, and organ failure.