For the treatment of renal malformation tumor, it involves the clinical manifestation, size and location of the malformation tumor, etc. The treatment methods are as follows: 1. If the diameter of the malformation tumor is 1-2cm and it is found by chance during physical examination, it is suggested that the patient should continue to observe; 2. If the malformation tumor increases progressively and there may be rupture and bleeding, it is suggested that the patient should be operated as soon as possible to avoid life-threatening hemorrhage from tumor rupture. For the misshapen tumor with diameter of 4-5cm, kidney-preserving surgery should be chosen as far as possible, either ordinary laparoscopic surgery or da Vinci surgery; 3. If the misshapen tumor of kidney is 15-30cm in diameter when it is found and has produced compression symptoms, such as lumbar pain and distension, patients are suggested to choose surgery at this time. Therefore, malformation tumor should be selected according to the patient’s clinical manifestations, tumor size and location to choose the appropriate treatment plan.