Immobile cilia syndrome is a multiple genetic disorder caused by defects in the structure of the cilia and is inherited in an autosomal recessive manner. The onset of immobile cilia syndrome is very early, often in newborns or early infants, and presents with airway obstruction and respiratory distress. Due to ciliary defects and impaired clearance, recurrent upper respiratory tract infections, chronic bronchitis or interstitial pneumonia may occur, resulting in atelectasis and bronchiectasis with symptoms such as coughing, coughing up thick sputum, hemoptysis, and dyspnea.