Pulmonary lymphangioleiomyomatosis is not a terminal disease, it is a clinically rare disease. Pulmonary lymphangioleiomyomatosis is a special kind of smooth muscle malignant hyperplasia and belongs to the immune system disease, not a malignant tumor, so it is not a terminal disease; it occurs most often in females around 30 years old, and the cause is unknown, and the symptoms usually show progressive dyspnea, recurrent spontaneous pneumothorax or/and celiac disease. Treatment is usually supportive, such as bronchodilatation, oxygenation, infection control, etc. Lung transplantation can be performed if necessary. It is recommended that patients should be detected and treated early so as not to delay the condition and cause irreversible damage.