High palatal arches are mostly seen in Marfan’s syndrome, mainly with elongated limbs, spider fingers (toes), arms extended flat with finger spacing greater than the length of the body, hands hanging down over the knees, upper body longer than the lower body. Long head deformity, narrow face, high palatal arch, large and low ears. Little subcutaneous fat, underdeveloped muscles, wrinkled skin on the chest, abdomen and arms. The muscle tone is low, with an inert body type. Ligaments, tendons and joint capsules are elongated and lax, and joints are hyperextended. Sometimes funnel chest, chicken chest, kyphosis, scoliosis, and spina bifida are seen. Cardiovascular lesions mainly invade the aorta, aortic valve and mitral valve and are the main cause of death. Since this disease is very characteristic, it can be described as a clear-cut disease. The disease can be demonstrated by a chain of genetic locus dominant inheritance in the family, as evidenced by increased urinary hydroxyproline excretion in the patient, which is an elastin fiber defect, also known as an abnormality of collagen metabolism. High palatal arch is the main manifestation of Marfan’s syndrome. The main danger of this disease is cardiovascular lesions, especially the combined aortic aneurysm, which should be detected early and treated early. The diagnosis can be made based on the clinical presentation of the three main signs of skeletal, ocular and cardiovascular changes and family history. Clinically, there are two types: those with all three main signs are called complete; those with only two are called incomplete. In the 1996 revised diagnostic criteria for Marfan’s syndrome, several major and minor criteria are listed in the skeleton, eyes, cardiovascular, lung, skin and body envelope, dura (spinal) membrane, and family genetic history, etc. In the absence of family or genetic history, more than two major criteria of different systems and more than three organs are required to confirm the diagnosis of Marfan’s syndrome. Early surgical repair of congenital cardiovascular lesions is advisable, and medical treatment of cardiac insufficiency and arrhythmias is appropriate. Once the diagnosis of a combined aortic aneurysm or heart valve closure insufficiency is confirmed, surgical treatment should be considered as appropriate, as medications cannot remove the condition. Because of the risk of rupture and bleeding from the aneurysm and the risk of death from heart failure from an insufficiently closed heart valve, experts recommend surgery despite the risks involved. In fact, with technological advances, the success rate of surgery is now above 90%. If a ruptured aortic coarctation aneurysm is indicated, surgery should be performed promptly.