The K-F ring refers to the corneal pigment ring, which has little effect on the health of the eye and the eyeball. It can usually be examined through a slit lamp microscope. These patients go to the ophthalmologist for an examination that is primarily an ancillary test to help determine if the patient has hepatomegaly. Corneal pigment rings are due to abnormal copper ion metabolism that deposits on the posterior surface of the cornea, creating a coppery-green ring-like appearance that can only be visualized under an ophthalmic slit lamp. The primary disease of corneal pigment ring is hepatomegaly, an autosomal recessive disorder that is clinically rare. Hepatomegaly can cause hepatic symptoms, neurologic symptoms, skin symptoms, and corneal changes. When corneal pigmentation ring appears, it is recommended to consult a doctor, follow the doctor’s instructions for further examination, find out the cause of the disease with the help of the doctor, and carry out targeted treatment or management.