Obviously, there is no growth acceleration during puberty, and the adult height is not more than 150cm; 2, the secondary sexual characteristics do not develop, there is primary amenorrhea, external genital dysplasia, the vulva can remain in the state of young breasts, sparse pubic and axillary hair, or even the lack of breasts, the breast does not develop, and the nipple spacing is wider; 3, there are special signs of body, such as neck shortness, neck webbing, elbow ectropion, and low hairline in the back, and there may be a nevus, and there may be a variety of internal organ malformations, and there are a variety of internal organ malformations in the combination. There may also be pigmented nevi, which may be combined with a variety of visceral malformations. Therefore, for congenital ovarian hypoplasia syndrome, comprehensive medical monitoring should be strengthened at all ages, especially paying attention to the pregnancy care of the mother.