Spinal cord embolism syndrome is a common congenital disorder of the central nervous system in children. Most of them will show some abnormal manifestations at the skin of the lumbosacral region at birth, such as dermatomal sinus and lipoma, which are easily ignored by parents or even medical personnel due to the lack of knowledge about them, and when the children grow up and show symptoms and then come to the surgery, the results are not very satisfactory. Therefore, early detection and treatment is particularly important. In this article, we provide some brief information about spinal cord embolism syndrome. Spinal cord tethering syndrome is a series of clinical syndromes caused by various congenital developmental abnormalities of the spinal cord. The spinal cord tethering is the lower end of the spinal cord (conus) that is restricted to the end of the spinal canal for various reasons, leaving it in a lower than normal position. Spinal cord embolism can be caused by spinal cord end filament tension, fatty spinal cord bulge, occult spina bifida, spinal cord splitting malformation, dermatomal sinus and dermatomal cysts, and even bladder bulge. Clinical manifestations Lumbosacral skin changes Lumbosacral skin bulge or depression, possibly with discharge or infection; hypertrichosis; recessive spina bifida, dermatomal sinus, spinal bulge, subcutaneous lipoma, etc. Kyphosis or scoliosis deformity Forked vertebrae, hemivertebrae and vertebral fusion, etc. Motor disorders of the lower extremities manifest as abnormal walking, weakness of the lower extremities, ankle deformation (clubfoot). Sensory disorders of the lower extremities manifest as abnormal sensation and pain in the lower extremities, perineum and low back. Urinary and fecal dysfunction Commonly manifested as urinary retention, difficulty in urination, urinary incontinence, frequent urination, less than normal volume each time, etc.; a few patients have constipation, constipation, or incontinence. Treatment Preferred surgical treatment, the purpose of surgery is to loosen the embolism of the spinal cord. Rehabilitation can be continued after surgery.