Cerebellar-retinal true hemangioma syndrome, also known as VonHippel-Lindau syndrome (disease), Hippel syndrome (disease), multiple vascular reticulocytoma syndrome, retinocerebellar hemangiomatosis, hereditary central nervous system hemangiomatosis, visceral cystic retinal hemangiomatosis, Hippel-Czermak syndrome, cerebellar reticuloangiomatosis , retinal angiomatosis, Lindau syndrome (disease), cystic retinal angiomatosis, cerebellar visceral angiomatosis, cerebellar retinal angiomatosis syndrome, Lindau tumor. How is cerebellar-retinal syndrome examined? The disease is more common in males. Neurological symptoms are extremely common, up to 90-100%. It starts in adults and lasts from a few weeks to several years. The presentation is the same as other cerebellar tumors, but it occurs late and progresses slowly, with significant nystagmus, cerebellar ataxia, and hypotonia. There are signs of cranial hypertension such as headache, vertigo, nausea, vomiting, optic papillar edema, and mental changes. Supratentorial hemangiomas are less common and have a clinical presentation similar to benign tumors of the cerebral hemispheres, which may still be present. It is to be differentiated from Joubert syndrome. This disease results in ataxia and balance disorders due to cerebellar earthworm dysplasia. The syndrome is autosomal recessive and can be diagnosed prenatally using ultrasound testing of the fetal cerebellum, but is often unsuccessful. Cerebellar cysts can be surgically removed to remove the hemangioma from the cyst wall. In cases of recurrent intraocular hemorrhage, laser irradiation, thermal coagulation, and freezing can be used to destroy the hemorrhagic vessels, and X-ray irradiation can also be tried, but it is necessary to protect the anterior end of the eye to prevent the occurrence of radioactive cataract. There are different views on the cause of cerebellar-retinal syndrome. In general, the cause of cerebellar-retinal syndrome is unknown. Other aspects do not exclude the influence of various aspects such as trauma. There is a benign congenital hemangioma in the brain – hemangioblastoma, also known as vascular reticulocytoma. It is usually located in one cerebellar hemisphere, mostly in the cerebellar earth or at the base of the fourth ventricle, and more rarely in the superior colliculus. Most hemangiomas are cystic in nature, but a few are parenchymal in nature and are combined with retinal hemangiomas.