Ectodermal Lobe Hypoplasia Syndrome is characterized by a widening of the forehead, a saddle-shaped collapsed nose, thick and prominent lips, a protruding chin, a lack of height in the lower third of the face, and a lack of teeth. Teeth, nasal mucosa, nervous system, hair, epidermis, skin glandular tissue and other tissues are derived from the ectodermal lobe, if the ectodermal lobe occurs congenital developmental disorders, it will cause a variety of tissues and structures of the developmental dysfunction or even deformity. This can lead to special facial features such as widening of the forehead, collapsed nose in the shape of a saddle, thick and protruding lips, protruding chin, insufficient height of the lower third of the face, and missing teeth. Early diagnosis and early treatment of exotropic hypoplasia syndrome can help patients to supplement some of their functions and regain confidence. Plastic surgery can be considered for patients with collapsed nasal bridge, and denture implantation can be used for patients with missing teeth to restore chewing function and facial aesthetics. If there is ectodermal hypoplasia syndrome, early diagnosis and its treatment should be made under the guidance of professional physicians to maximize the restoration of the patient’s function.