Cerebrospinal bulge is not hereditary and is mainly caused by a low perinatal intake of folic acid. The main cause of this type of disease is due to dominant craniosynostosis, a defect in the skull that causes the brain tissue to protrude through the defect onto the surface of the scalp. Patients in this category should be operated on before the age of one year as soon as their condition allows. If early surgery is not possible, care should be taken to protect the skin at the site of the bulge to prevent infection and breakage. The aim of surgery is to remove the wall of the bulging sac and to protect the neurological function. The main purpose of surgery for those with a skull base split is to repair it to prevent cerebrospinal fluid leakage and to prevent pneumocranial and intracranial infections. If hydrocephalus is present during surgery, cerebrospinal fluid shunts should be performed first.