Focal nodular hyperplasia of the liver (FNH) is a rare benign lesion of the liver, the cause of which is still unclear. Due to recent advances in imaging techniques, reports of focal nodular hyperplasia of the liver have gradually increased. Most patients do not have clinical symptoms and are mostly found incidentally during physical examination or during medical examination for other problems. There are no characteristic abnormalities on hematological examination. Enhanced CT and MRI help to clarify the diagnosis. The typical presentation is significant homogeneous enhancement in the arterial phase, non-enhancement in the center of the nodule due to the presence of a central scar, and similar density to the surrounding liver parenchyma in the delayed phase. Since no evidence of malignancy has been found in focal nodular hyperplasia of the liver, focal nodular hyperplasia of the liver with a clear diagnosis can be observed regularly without surgery; for those with an unclear diagnosis that cannot exclude malignancy and those with symptoms of compression, surgical resection can be considered. The prognosis is good.