The treatment of aneurysmal dermatofibrosarcoma is based on surgery, supplemented by radiotherapy, chemotherapy alternative, and also targeted therapy. Treatment methods are as follows: 1. Surgery: the local recurrence rate of tumor is high, and local infiltration is strong, but distant metastasis rarely occurs, so the treatment is mainly surgery, and to expand the resection, that is, to remove 3cm of normal tissue around the tumor; after surgery, according to the specific situation, supplemented with radiation therapy, which can further reduce the recurrence rate; 2. Targeted therapy: aneurysmal dermatofibrosarcoma has a special target expression, at present Oral Imatinib can be used to treat the target. Aneurysmal dermatofibrosarcoma is a type of fibrous sarcoma, which mostly occurs in adults. The tumor grows mainly on the ventral side of the limbs and trunk, but rarely on the head and neck, palms and feet. The clinical manifestation is a skin nodule that initially is the same color as the skin, and then the nodule grows progressively larger and more elevated, forming a purplish-red nodule called an augmentation dermatofibrosarcoma.