Children with glutaric acidemia type 1 are given a special formula that removes lysine. It is an amino acid metabolism disorder formula. Glutaric acidemia type 1 is an autosomal recessive genetic metabolic disorder of lysine, hydroxylysine and tryptophan metabolism disorders, lysine intake should be gradually reduced with the age of the child. <6-month-old children not more than 100mg/(kg.d):6~12-month-old children not more than 90mg/(kg.d);1-3-year-old children about 60~80mg/(kg.d):to 6 years old to reduce to 50~60mg/(kg.d);Lysine-free, low-tryptophan amino acid powder dosage in the <12-month-old children about 0.8~1.3g/( kg-d); after 1 year of age it is generally 0.8g/(kg.d). Glutaric acidemia type 1 children need to limit the intake of lysine, if the consumption of ordinary milk powder will lead to aggravation of the child’s condition, it is recommended that under the guidance of the physician to use the appropriate milk powder.