Lymphangioleioma in children is usually asymptomatic in its early stages and does not cause any discomfort, except that parents notice small localized lumps in the child such as the head and neck, trunk, and extremities, which can be either soft or relatively firm masses that are related to the type of lymphangioleioma. Lymphangioleioma increases in size as the infant ages and progresses to deeper tissues. If it encroaches on the surrounding nerve tissue, it can affect the normal physiological function of the affected area, and if it compresses the trachea, it can lead to asphyxia, and if it compresses the intestine, it can lead to intestinal obstruction or even intestinal torsion.