Umbilical ureteral remnants are umbilical ureteral cysts presenting as cystic masses in the lower abdomen medially, not changing with body position and superficially located in close relationship to the abdominal wall. Large umbilical ureteral cysts resemble intra-abdominal tumors and can compress the intestine, causing abdominal pain and other symptoms. They can also become abscesses due to secondary infection. Both abscesses or cysts can rupture and perforate outside the abdomen, or rupture into the bladder or into the abdominal and pelvic cavities. According to clinical examination, superficial cystic swellings in the subumbilical region vary in size, with the larger ones being palpable and mostly asymptomatic. In the case of secondary infection, a local inflammatory response is seen, and the diagnosis can be clearly established by combining ultrasound, CT, cystography and other imaging examinations. Ultrasound and CT are relatively easy to detect abnormalities in the umbilical ureter, and both can clearly show the type of umbilical ureter remnants. However, ultrasound and CT performance are more difficult to differentiate between infected umbilical ureter and umbilical ureteral tumor. Both infected umbilical ureter and umbilical ureteral tumor appear as strongly echogenic areas on ultrasound; on CT they appear as thick-walled cysts and diffuse attenuation, which makes it difficult to separate the two. Fine needle aspiration and cyst drainage have implications for both disease diagnosis and treatment planning. Since any part of the residual umbilical ureter can become cancerous, all types of congenital abnormal umbilical ureteral disease, once diagnosed, should be removed as soon as possible after infection control, and patients with encopresis, urethral stricture, and urethral valve disease should be pre-treated. Some scholars also believe that umbilical ureteral diverticula should be operated only when it is complicated by stones, infection or malignant changes. In this group of patients, all of whom were adults, the umbilical ureteral malformation was complicated by infection, stones and/or tumors. Due to the long duration of the disease and the lack of timely diagnosis and treatment, some patients had led to obstructive renal impairment or umbilical ureteral carcinoma with serious consequences. With surgical treatment, most of them have good treatment results. We believe that raising clinicians’ awareness of this disease and early surgical management after diagnosis is the key to cure this disease, which is not effective once cancer occurs. Umbilical ureteral malformations may have no clear clinical manifestations in the absence of other complications, but some may present with localized vague pain or urinary frequency due to compression of the surrounding tissues by the enlarged lumen or cyst. Common umbilical ureteral diseases include infections, stones and tumors.