An ectopic pancreas is a congenital embryonic developmental abnormality that has no anatomical or vascular connection to the normal pancreas. The common site of ectopic pancreas is the upper gastrointestinal tract. It accounts for 75% of cases in the stomach, followed by the duodenum and jejunum. Ectopic pancreas does not occur in the colon. Gastric ectopic pancreas is usually asymptomatic. When there is inflammation or bleeding at the site of the lesion, it causes corresponding nonspecific GI symptoms. The ectopic pancreas occasionally causes pyloric obstruction and small bowel obstruction, producing the corresponding signs and symptoms. Gastric ectopic pancreas is located in the submucosa of the digestive tract, and gastroscopy reveals a round or oval submucosal mass with regular margins and intact mucosa. More than half of the gastric ectopic pancreas is seen to have an umbilical-like depression in the middle of the lesion, which is caused by the ducts under it. Gastroscopy is often performed because of other indications and the ectopic pancreas is an accidental finding. Sometimes small masses in the gastrointestinal wall, yellow or white in color, are found during epigastric surgery and pathologically diagnosed as ectopic pancreas. This shows that the ectopic pancreas that can be detected in clinical work is really only a small fraction of the actual ectopic pancreas that exists. The small ectopic pancreas often has no secretory function, and the ectopic pancreas with secretory function can form cystic lesions. Malignant degeneration of the gastric ectopic pancreas is rare. Gastric ectopic pancreas is usually asymptomatic and rarely carcinogenic, plus many ectopic pancreases are in fact undetected. Therefore, it is recommended that cases smaller than 2 cm that are proposed to be diagnosed as ectopic pancreas by ultrasound endoscopy may not be resected and only regular review and follow-up should be done to reduce the patient’s injury and financial burden. For masses larger than 2 cm in diameter, surgical resection is recommended when the diagnosis is difficult to confirm preoperatively. However, if the intraoperative diagnosis of ectopic pancreas is proposed, the extent of gastrectomy need not be large.