In pediatric neurosurgery, fibrous dysplasia is commonly found in the base of the skull, such as the butterfly bone and sieve bone, and develops slowly. For most patients, a detailed evaluation is needed, including ophthalmologic examination of the visual field and fundus, and CT scan of the skull base. Based on the detailed examination, most patients need to be monitored dynamically, and surgery is required only if symptoms of vision loss occur. The disease progresses slowly, and many lesions stop progressing after puberty. However, parents of patients need to be careful to rule out McCune-Albright syndrome, where these children will have café-au-lait spots, may have had fractures, and may have symptoms of endocrine disorders such as hyperthyroidism, acromegaly, and gigantism.