In principle, umbilical ureteral cysts should be treated by surgical excision to avoid subsequent recurrent umbilical infections, urinary tract infections or localized cyst infections that cause redness, swelling, pain and other discomfort. Normal umbilical ureter can degenerate after birth, but if it does not degenerate completely, umbilical ureteral cyst, umbilical ureteral fistula or its ureteral sinus may appear. Umbilical ureteral cysts tend to occlude at the umbilical and bladder ends, with cystic changes caused by secretions or local contamination in between. Some patients may be asymptomatic and most may have a subumbilical mass or discomfort such as redness, swelling or pain. Some patients can have recurrent umbilical infections of unknown origin, and the umbilical ureteral cysts are found on physical examination. If the cyst is small without any conscious symptoms and is found occasionally on physical examination, it can be observed clinically. If the cyst increases in size during observation and symptoms of umbilical infection or recurrent urinary tract infections appear, surgical removal is recommended. For patients with larger cysts with recurrent infection episodes, surgical excision is recommended as soon as they are detected to cure them completely.