Repeat ureteral malformation is a relatively rare congenital malformation in urology, which usually has no obvious conscious symptoms. Is surgery required for repeat ureteral malformation combined with urinary tract stones? What is the treatment method? It depends on the size and location of the stone, the degree of obstruction, and the kidney function. If the size of the stone is small, it can be treated conservatively first. For patients with kidney stones of 2 cm or more that must be treated surgically, there is no uniform treatment plan, and the choice of treatment is often based on the drainage of the affected kidney, the size of the stone and the experience of the doctor. When repeat kidney combined with upper urinary tract stone undergoes nephrotomy for stone extraction, it is difficult to remove the stone surgically due to anatomical reasons such as urinary tract malformation, while minimally invasive percutaneous nephrolithotomy for repeat kidney ureteral malformation combined with kidney stone treatment has short operation time, small trauma, less bleeding and high stone removal rate, which can minimize the damage to the kidney.