Medulloblastoma, first reported by Bailey and Cushing in 1925, is an intracranial malignancy that occurs in children and is one of the most malignant neuroepithelial tumors of the central nervous system. It is thought to occur as a result of the failure of the primitive myeloid epithelium to continue to differentiate. This tumor, which originates from embryonic remnant cells, can occur anywhere in the brain tissue, but the vast majority grows in the cerebellar earthworms above the roof of the fourth ventricle. The main manifestations are increased intracranial pressure and ataxia and other cerebellar symptoms, often diplopia and various cerebral neurological disorders, and cervical ankylosis and oblique neck in case of cerebellar tonsillar herniation. The prognosis has improved significantly over the last decade or so with the advancement of comprehensive therapies.