Craniopharyngioma is a congenital tumor, accounting for about 5% of intracranial tumors, mostly seen in children and adolescents, more in males than females. Most of the tumors are located in the suprasellar region, and may develop in the direction of the third ventricle, hypothalamus, interpeduncular pool, paracranial lobe, both temporal lobes, frontal lobe base and inner saddle, etc. They compress the optic nerve and optic cross, block the cerebrospinal fluid circulation and lead to hydrocephalus. Most of the tumors are cystic in nature, and the cystic fluid is yellowish brown or dark brown in color, containing a large amount of cholesterol crystals. The tumor wall is covered with calcified plaques. Microscopically the tumor cells mainly consist of squamous or columnar epithelial cells, some of which are arranged into tooth enamel organ-like structures. The main manifestations are visual impairment, visual field defects, enuresis, obesity, and growth retardation. Adult men have sexual dysfunction and women have menstrual irregularities. Late stage can have symptoms of intracranial hypertension. In addition to the enlargement and shallowing of the pterygoid saddle, calcification in the suprasellar region can be seen on cranial radiographs. Treatment is mainly surgical.