Bou-ga syndrome: a post-hepatic portal hypertension characterized by obstructive lesions of the hepatic veins and/or the inferior vena cava of its opening with or without hypertension of the inferior vena cava. There are three types of the disease, namely, limited stenosis or obstructive (type I), diffuse stenosis or obstructive (type II), and obstructive hepatic vein (type III) with predominantly inferior vena cava septum. Type I accounts for about 57%; type II accounts for about 38%; and type III accounts for about 5%. The age of onset of the disease varies depending on the cause of onset, because of congenital developmental abnormalities, the earliest onset is 2.5 years old. The earliest onset is 2.5 years old, but it occurs mostly between the ages of 20-40. The age of onset is later in cases of acquired causes. In cases of hepatic vein obstruction alone, symptoms of portal hypertension are predominant, while in cases of combined inferior vena cava obstruction, symptoms of both portal hypertension and inferior vena cava obstruction syndrome are present. In late stage, due to severe ascites, repeated laparotomies for abdominal decompression to relieve symptoms, protein loss, and finally death due to severe malnutrition, gastrointestinal hemorrhage from ruptured esophageal varices, or liver and kidney failure.